Heart Defects, CongenitalNCT00115934
Comparison of Two Types of Shunts in Infants With Single Ventricle Defect Undergoing Staged Reconstruction--Pediatric Heart Network
A study testing Blalock-Taussig pulmonary artery shunt and Right ventricular to pulmonary artery shunt in people with Heart Defects, Congenital, run by Carelon Research at 13 sites in 2 countries.
Trial summary
This trial will evaluate the efficacy and safety of the modified Blalock-Taussig shunt (MBTS) compared to the right ventricle to pulmonary artery (RV-to-PA) shunt; compare the effect of the MBTS to that of the RV-to-PA shunt on the incidence of death or cardiac transplantation at 12 months post randomization; and… Read more about this study
- Who is it for?
- Any age
- Conditions the study is for
- Heart Defects, Congenital
- What is being tested?
- Blalock-Taussig pulmonary artery shunt and Right ventricular to pulmonary artery shunt
- Type of treatment
- Surgery or procedure
- Could I receive a placebo?
- No, everyone receives an active treatment
- How many people
- 555 participants
- Where
- 13 sitesin 2 countries
- Study dates
- May 2005to Oct 2009
- Phase
- Interventional
- Are there results?
- Yes, posted in the registrySummary in the doctors' view
Key requirements
Who can take part, as listed by the sponsor. Only the study team can confirm whether you are eligible, so take this list to your doctor.
- Ages Any age
- All sexes
- No healthy volunteers
- Child, Adult, Older adult
Who may be able to join
- Diagnosis of hypoplastic left heart syndrome or related single, morphologic right ventricle anomaly
- Planned Norwood procedure
- Informed consent of parent(s) or legal guardian
Who cannot join
- Single, morphologic left ventricle anomaly
- Preoperative identification of anatomy rendering either an MBTS or an RV-to-PA shunt technically impossible
- Any major congenital abnormality (i.e., congenital diaphragmatic hernia, tracheoesophageal fistula) or acquired extra-cardiac disorder (e.g., meconium aspiration with need for high frequency ventilation, persistent renal failure requiring dialysis) that, in the opinion of the investigator, could independently affect the likelihood of the subject meeting the primary endpoint
Trial locations and contacts
13 sites in 2 countries.
13 sites in 2 countries
United States12 sites
University of Michigan Health System/Mott Hospital
Ann Arbor, Michigan, 48109
Children's Healthcare of Atlanta at Egleston
Atlanta, Georgia, 30033
Children's Hospital Boston
Boston, Massachusetts, 02115
Medical University of South Carolina
Charleston, South Carolina, 29425
Cincinnati Children's Hospital Medical Center
Cincinnati, Ohio, 45229
Duke University Medical Center
Durham, North Carolina, 27710
Children's Hospital of Los Angeles
Los Angeles, California, 90027
Children's Hospital of Wisconsin
Milwaukee, Wisconsin, 53226
Columbia College of Physicians and Surgeons
New York, New York, 10032
Children's Hospital of Philadelphia
Philadelphia, Pennsylvania, 19104
Cardiac Surgical Associates
St. Petersburg, Florida, 33709
Alfred I. duPont Hospital for Children
Wilmington, Delaware, 19899
About this study
Official title: Trial of Right Ventricular Versus Modified Blalock-Taussig Shunt in Infants With Single Ventricle Defect Undergoing Staged Reconstruction (A Trial Conducted by the Pediatric Heart Network)
This trial will evaluate the efficacy and safety of the modified Blalock-Taussig shunt (MBTS) compared to the right ventricle to pulmonary artery (RV-to-PA) shunt; compare the effect of the MBTS to that of the RV-to-PA shunt on the incidence of death or cardiac transplantation at 12 months post randomization; and compare the effect of the two shunts on intensive care unit (ICU) morbidity, unintended cardiovascular interventional procedures, right ventricular function, tricuspid valve regurgitation, pulmonary artery growth, and neurodevelopmental outcome.
Read the detailed description
BACKGROUND:
Hypoplastic left heart syndrome (HLHS) and related single right ventricle anomalies are the highest risk congenital cardiovascular malformations. Surgical repair begins with the Norwood procedure during the newborn period, a stage II procedure at 4 to 6 months of age, and Fontan procedure at 18 to 36 months. The Norwood procedure remains one of the highest risk procedures in congenital heart surgery. A few small nonrandomized studies of a novel approach to the Norwood procedure have reported improved outcomes. This new approach uses a RV-to-PA shunt to provide pulmonary blood flow rather than the standard MBTS. This multi-center, randomized clinical trial will evaluate early and intermediate-term outcomes for patients undergoing a Norwood procedure with either the RV-to-PA shunt or the MBTS.
This study has been approved by the Institutional Review/Research Ethics Boards of all participating clinical centers:
Hospital for Sick Children, Toronto, Canada
Children's Hospital Boston, Boston, MA
Columbia College of Physicians and Surgeons, New York, NY
Children's Hospital of Philadelphia, Philadelphia, PA
Duke University Medical Center, Durham, NC
Brody School of Medicine at East Carolina University, Greenville, NC
Wake Forest Baptist Medical Center, Winston Salem, NC
Medical University of South Carolina, Charleston, SC
Children's Hospital of Wisconsin, Milwaukee, WI
University of Michigan, Ann Arbor, MI
Cincinnati Children's Hospital Medical Center, Cincinnati, OH
Children's Hospital of Los Angeles, Los Angeles, CA
Egleston Children's Hospital, Emory University, Atlanta, GA
Congenital Heart Institute of Florida, University of South Florida, St. Petersburg, FL
Alfred I. duPont Hospital for Children, Wilmington, DE
DESIGN NARRATIVE:
This is a prospective, randomized clinical trial of the RV-to-PA shunt versus MBTS in patients undergoing a Norwood procedure.
- Conditions
- Heart Defects, Congenital
- Being tested
- Blalock-Taussig pulmonary artery shunt, Right ventricular to pulmonary artery shunt
- Medical subject headings
- Heart Defects, Congenital
What participants receive
What participants receive. In a randomised study each person is assigned to one group by chance.
Blalock-Taussig pulmonary artery shuntProcedure or surgery
Also called MBTS procedure
Performed at stage I palliative surgery for babies born with HLHS
Right ventricular to pulmonary artery shuntProcedure or surgery
Also called RV to PA or Sano procedure
Performed at stage I palliative surgery for babies born with HLHS
| Study group | Role | What they receive |
|---|---|---|
| MBTS | Active comparator | Blalock-Taussig pulmonary artery shunt Receives: Procedure: Blalock-Taussig pulmonary artery shunt |
| RVPAS | Active comparator | Right ventricular to pulmonary artery shunt Receives: Procedure: Right ventricular to pulmonary artery shunt |
What is being measured
The primary outcome is the main question the study is designed to answer.
Proportion of Patients Who Died or Received a Heart Transplant
The primary outcome was the proportion of patients who died or had cardiac transplantation 12 months after randomization.
Measured: Measured at 12 months
Secondary outcomes (16)
Proportion of Deaths or Heart Transplants Over Time From Randomization to the End of the Trial
This secondary outcome was the proportion of deaths or cardiac transplantation over time from randomization to the end of the trial.
Measured: From Randomization to the End of the Trial, an average of 32 months
Echocardiographic Measures of Heart Size and Function: Right Ventricle (RV) End-diastolic Volume Indexed to Body Surface Area (BSA)
Right ventricular end-diastolic volume indexed to BSA^1.3. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV End-diastolic Volume Indexed to BSA
Right ventricular end-diastolic volume indexed to BSA^1.3. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV End-diastolic Volume Indexed to BSA
Right ventricular end-diastolic volume indexed to BSA^1.3. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured at 14 months of age
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Right ventricular end-systolic volume indexed to BSA. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Right ventricular end-systolic volume indexed to BSA^1.3. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Right ventricular end-systolic volume indexed to BSA^1.3. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured at 14 months of age
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Right ventricular ejection fraction: 100 x (RV end-diastolic volume - RV end-systolic volume)/RV end-diastolic volume. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Right ventricular ejection fraction: 100 x (RV end-diastolic volume - RV end-systolic volume)/RV end-diastolic volume. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Right ventricular ejection fraction: 100 x (RV end-diastolic volume - RV end-systolic volume)/RV end-diastolic volume. Echocardiograms were performed at time points relative to the two palliative surgeries (post-Norwood and pre-Stage II) as well as at the specific time point of 14 months of age.
Measured: Measured at 14 months of age
Angiographic Findings: Left Pulmonary Artery Size
Diameter of distal left pulmonary artery. Angiograms were performed at the time points relative to the second palliative surgery (pre-Stage II).
Measured: Measured pre-stage II surgery, on average 26 days prior to stage II palliation
Angiographic Findings: Right Pulmonary Artery Size
Diameter of distal right pulmonary artery. Angiograms were performed at the time points relative to the second palliative surgery (pre-Stage II).
Measured: Measured pre-stage II surgery, on average 26 days prior to stage II palliation
Unintended Cardiovascular Interventional Procedures
Unintended cardiovascular procedures included balloon dilation of the shunt or branch pulmonary arteries, stent placement in the shunt or branch pulmonary arteries, shunt revision, crossover between MBTS and RVPAS shunt, balloon dilation, stent placement or surgical revisions of the neo-aorta, and pulmonary artery reconstructions, other than those undertaken as a standard component of the stage II procedure. The number of cardiovascular procedures was analyzed; trial participants may have had more than one unintended cardiovascular. procedure.
Measured: From Randomization to 12 months
Complications: Total Number Experienced During Norwood Hospitalization
Complications, reported as 'Other Adverse Events' in the safety section, are those adverse events that were not considered serious. Many normal peri-operative occurrences meet the standard criteria of an adverse event; therefore, for this trial a serious adverse event was (a) death, (b) acute shunt failure requiring intervention, (c) cardiac arrest requiring CPR and medications, (d) cardiopulmonary insufficiency requiring ECMO, (e) cardiovascular re-operation (unplanned), (f) necrotizing enterocolitis requiring laparotomy, and (g) any event considered by the study investigator as serious.
Measured: Norwood Hospitalization, an average of 36 days
Complications: Total Number Experienced From Norwood Discharge to Stage II Discharge
Complications, reported as 'Other Adverse Events' in the safety section, are those adverse events that were not considered serious. Many normal peri-operative occurrences meet the standard criteria of an adverse event; therefore, for this trial a serious adverse event was (a) death, (b) acute shunt failure requiring intervention, (c) cardiac arrest requiring CPR and medications, (d) cardiopulmonary insufficiency requiring ECMO, (e) cardiovascular re-operation (unplanned), (f) necrotizing enterocolitis requiring laparotomy, and (g) any event considered by the study investigator as serious.
Measured: From Norwood Discharge to Stage II discharge, an average of 4.2 months
Complications: Total Number Experienced From Stage II Discharge to 14 Months of Age
Complications, reported as 'Other Adverse Events' in the safety section, are those adverse events that were not considered serious. Many normal peri-operative occurrences meet the standard criteria of an adverse event; therefore, for this trial a serious adverse event was (a) death, (b) acute shunt failure requiring intervention, (c) cardiac arrest requiring CPR and medications, (d) cardiopulmonary insufficiency requiring ECMO, (e) cardiovascular re-operation (unplanned), (f) necrotizing enterocolitis requiring laparotomy, and (g) any event considered by the study investigator as serious.
Measured: From Stage II Discharge to 14 Months of Age, an average of 8.9 months
Timeline
From the start of the study to its completion; the mark is today. Estimated dates are the sponsor’s plan.
- First posted27 Jun 2005 (estimated)
- Study startMay 2005
- Primary completionSep 2009
- Study completionOct 2009
Resources
- Official record on ClinicalTrials.govThe registry entry this page is built from, with its full change history.
- Posted resultsParticipant flow, outcome measures and adverse events reported by the sponsor.
- Publications (38)Papers the sponsor has linked to this study.
- Other trials for Heart Defects, CongenitalStudies of the same condition, open and under way.
- What the trial phases meanHow a treatment moves from first tests in people to approval.
More details
For doctors and researchers: how the study is designed, who runs it, and its registry IDs.
Study design
- Study type
- Interventional
- Phase
- Phase N/A
- Primary purpose
- Treatment
- Allocation
- Randomised
- Intervention model
- Parallel groups
- Masking
- None (open label)
- Enrolment
- 555 participants (actual)
Sponsor and investigators
- Lead sponsor
- Carelon Research
- Sponsor type
- University, hospital or other
- Collaborators
- National Heart, Lung, and Blood Institute (NHLBI), Pediatric Heart Network
- Responsible party
- Sponsor
- Investigators
- Julie E Miller, MPH, Principal investigator, New England Research Institutes, Watertown, MA
IDs, dates and publications
- ClinicalTrials.gov ID
- NCT00115934
- Sponsor's protocol ID
- 194
- Other IDs
- U01HL068270, U01HL068269, U01HL068279, U01HL068281, U01HL068285, U01HL068288, U01HL068290, U01HL068292
- Status last verified
- Aug 2013
- First submitted
- 26 Jun 2005
- Last updated
- 11 Mar 2025
- Results posted
- Yes, on ClinicalTrials.gov
- Data monitoring committee
- Yes
Publications
Ohye RG, Gaynor JW, Ghanayem NS, Goldberg CS, Laussen PC, Frommelt PC, Newburger JW, Pearson GD, Tabbutt S, Wernovsky G, Wruck LM, Atz AM, Colan SD, Jaggers J, McCrindle BW, Prakash A, Puchalski MD, Sleeper LA, Stylianou MP, Mahony L; Pediatric Heart Network Investigators. Design and rationale of a randomized trial comparing the Blalock-Taussig and right ventricle-pulmonary artery shunts in the Norwood procedure. J Thorac Cardiovasc Surg. 2008 Oct;136(4):968-75. doi: 10.1016/j.jtcvs.2008.01.013. Epub 2008 May 19.
PubMed 18954638Johnson JN, Ansong AK, Li JS, Xu M, Gorentz J, Hehir DA, del Castillo SL, Lai WW, Uzark K, Pasquali SK. Celiac artery flow pattern in infants with single right ventricle following the Norwood procedure with a modified Blalock-Taussig or right ventricle to pulmonary artery shunt. Pediatr Cardiol. 2011 Apr;32(4):479-86. doi: 10.1007/s00246-011-9906-y. Epub 2011 Feb 18.
PubMed 21331516Virzi L, Pemberton V, Ohye RG, Tabbutt S, Lu M, Atz TC, Barnard T, Dunbar-Masterson C, Ghanayem NS, Jacobs JP, Lambert LM, Lewis A, Pike N, Pizarro C, Radojewski E, Teitel D, Xu M, Pearson GD. Reporting adverse events in a surgical trial for complex congenital heart disease: the Pediatric Heart Network experience. J Thorac Cardiovasc Surg. 2011 Sep;142(3):531-7. doi: 10.1016/j.jtcvs.2010.11.052. Epub 2011 Mar 12.
PubMed 21397260Atz AM, Travison TG, Williams IA, Pearson GD, Laussen PC, Mahle WT, Cook AL, Kirsh JA, Sklansky M, Khaikin S, Goldberg C, Frommelt M, Krawczeski C, Puchalski MD, Jacobs JP, Baffa JM, Rychik J, Ohye RG; Pediatric Heart Network Investigators. Prenatal diagnosis and risk factors for preoperative death in neonates with single right ventricle and systemic outflow obstruction: screening data from the Pediatric Heart Network Single Ventricle Reconstruction Trial( *). J Thorac Cardiovasc Surg. 2010 Dec;140(6):1245-50. doi: 10.1016/j.jtcvs.2010.05.022. Epub 2010 Jun 18.
PubMed 20561642Ohye RG, Sleeper LA, Mahony L, Newburger JW, Pearson GD, Lu M, Goldberg CS, Tabbutt S, Frommelt PC, Ghanayem NS, Laussen PC, Rhodes JF, Lewis AB, Mital S, Ravishankar C, Williams IA, Dunbar-Masterson C, Atz AM, Colan S, Minich LL, Pizarro C, Kanter KR, Jaggers J, Jacobs JP, Krawczeski CD, Pike N, McCrindle BW, Virzi L, Gaynor JW; Pediatric Heart Network Investigators. Comparison of shunt types in the Norwood procedure for single-ventricle lesions. N Engl J Med. 2010 May 27;362(21):1980-92. doi: 10.1056/NEJMoa0912461.
PubMed 20505177Ohye RG, Devaney EJ, Hirsch JC, Bove EL. The modified Blalock-Taussig shunt versus the right ventricle-to-pulmonary artery conduit for the Norwood procedure. Pediatr Cardiol. 2007 Mar-Apr;28(2):122-5. doi: 10.1007/s00246-006-1449-2. Epub 2007 Feb 16.
PubMed 17308942Hill KD, Kang L, Wang Q, Newburger JW, Gaynor JW, Burns KM, Williams R, Trachtenberg F, McCrindle BW, Graham EM, Pizarro C, Ashfaq A, Souza A, Kuo JA, Ilardi D, Schumacher KR, Hong H, Goldberg CS; Pediatric Heart Network Investigators. Single-Ventricle Disease: Long-Term Outcomes and Global Morbidity in the Single Ventricle Reconstruction Trial. J Am Coll Cardiol. 2026 Jun 9;87(22):3114-3133. doi: 10.1016/j.jacc.2026.01.049. Epub 2026 Mar 11.
PubMed 41811273Cnota JF, Chowdhury SM, Floh A, Gongwer R, Goot BH, Jacobs JP, Jolley MA, Kirmani S, LaPar DJ, Levine JC, Lewis AB, Pignatelli RH, Pizarro C, Slesnick TC, Thorsson T, Trachtenberg F, Truong DT, Newburger JW, Frommelt PC; Pediatric Heart Network Investigators. Tricuspid Regurgitation and Impact of Surgical Valve Intervention in the Single Ventricle Reconstruction Trial. Pediatr Cardiol. 2026 Feb 18. doi: 10.1007/s00246-025-04122-x. Online ahead of print.
PubMed 41706109Mahle WT, Keesari R, Trachtenberg F, Newburger JW, Lim H, Edelson J, Jeewa A, Lal A, Kindel SJ, Burns KM, Lang S, Bainton J, Carboni M, Villa CR, Richmond M, Henderson H, Menteer J, Pizarro C, Goldberg CS. School age and adolescent heart failure following the Norwood procedure. J Heart Lung Transplant. 2024 Mar;43(3):453-460. doi: 10.1016/j.healun.2023.10.012. Epub 2023 Oct 20.
PubMed 37866470Dolgner SJ, Tjoeng YL, Chan T. Analysis of the Single Ventricle Reconstruction Trial Using Restricted Mean Survival Time and Shunt Type Received. J Am Heart Assoc. 2022 Sep 20;11(18):e025978. doi: 10.1161/JAHA.122.025978. Epub 2022 Sep 8. No abstract available.
PubMed 36073629Miller TA, Ghanayem NS, Newburger JW, McCrindle BW, Hu C, DeWitt AG, Cnota JF, Tractenberg FL, Pemberton VL, Wolf MJ, Votava-Smith JK, Fifer CG, Lambert LM, Shah A, Graham EM, Pizarro C, Jacobs JP, Miller SG, Minich LL; Pediatric Heart Network Investigators. Gestational Age, Birth Weight, and Outcomes Six Years After the Norwood Procedure. Pediatrics. 2019 May;143(5):e20182577. doi: 10.1542/peds.2018-2577. Epub 2019 Apr 12.
PubMed 30979811Frommelt PC, Hu C, Trachtenberg F, Baffa JM, Boruta RJ, Chowdhury S, Cnota JF, Dragulescu A, Levine JC, Lu J, Mercer-Rosa L, Miller TA, Shah A, Slesnick TC, Stapleton G, Stelter J, Wong P, Newburger JW. Impact of Initial Shunt Type on Echocardiographic Indices in Children After Single Right Ventricle Palliations. Circ Cardiovasc Imaging. 2019 Feb;12(2):e007865. doi: 10.1161/CIRCIMAGING.118.007865.
PubMed 30755054Mahle WT, Hu C, Trachtenberg F, Menteer J, Kindel SJ, Dipchand AI, Richmond ME, Daly KP, Henderson HT, Lin KY, McCulloch M, Lal AK, Schumacher KR, Jacobs JP, Atz AM, Villa CR, Burns KM, Newburger JW; Pediatric Heart Network Investigators. Heart failure after the Norwood procedure: An analysis of the Single Ventricle Reconstruction Trial. J Heart Lung Transplant. 2018 Jul;37(7):879-885. doi: 10.1016/j.healun.2018.02.009. Epub 2018 Feb 16.
PubMed 29571602Newburger JW, Sleeper LA, Gaynor JW, Hollenbeck-Pringle D, Frommelt PC, Li JS, Mahle WT, Williams IA, Atz AM, Burns KM, Chen S, Cnota J, Dunbar-Masterson C, Ghanayem NS, Goldberg CS, Jacobs JP, Lewis AB, Mital S, Pizarro C, Eckhauser A, Stark P, Ohye RG; Pediatric Heart Network Investigators. Transplant-Free Survival and Interventions at 6 Years in the SVR Trial. Circulation. 2018 May 22;137(21):2246-2253. doi: 10.1161/CIRCULATIONAHA.117.029375. Epub 2018 Feb 1.
PubMed 29437119Bucholz EM, Sleeper LA, Newburger JW. Neighborhood Socioeconomic Status and Outcomes Following the Norwood Procedure: An Analysis of the Pediatric Heart Network Single Ventricle Reconstruction Trial Public Data Set. J Am Heart Assoc. 2018 Feb 2;7(3):e007065. doi: 10.1161/JAHA.117.007065.
PubMed 29420218
Study at a glance
From the registry record, last updated by the sponsor on 11 Mar 2025. Recruitment status is as the sponsor reported it: confirm with the study team.
- Official title
- Trial of Right Ventricular Versus Modified Blalock-Taussig Shunt in Infants With Single Ventricle Defect Undergoing Staged Reconstruction (A Trial Conducted by the Pediatric Heart Network)
- ClinicalTrials.gov ID
- NCT00115934
- Acronym / sponsor ID
- 194
- Conditions
- Heart Defects, Congenital
- Study type
- Interventional
- Recruitment status
- Completed
- Enrolment
- 555 participants (actual)
- Lead sponsor
- Carelon ResearchUniversity, hospital or other
- Collaborators
- National Heart, Lung, and Blood Institute (NHLBI), Pediatric Heart Network
- Study start
- May 2005
- Primary completion
- Sep 2009 (actual)
- Study completion
- Oct 2009 (actual)
- First posted
- 27 Jun 2005 (estimated)
- Results
- Posted 27 Jun 2011
Clinical summary
The research question as the sponsor registered it. This describes what the study plans to test, not what it found.
This trial will evaluate the efficacy and safety of the modified Blalock-Taussig shunt (MBTS) compared to the right ventricle to pulmonary artery (RV-to-PA) shunt; compare the effect of the MBTS to that of the RV-to-PA shunt on the incidence of death or cardiac transplantation at 12 months post randomization; and compare the effect of the two shunts on intensive care unit (ICU) morbidity, unintended cardiovascular interventional procedures, right ventricular function, tricuspid valve regurgitation, pulmonary artery growth, and neurodevelopmental outcome.
Detailed description
BACKGROUND:
Hypoplastic left heart syndrome (HLHS) and related single right ventricle anomalies are the highest risk congenital cardiovascular malformations. Surgical repair begins with the Norwood procedure during the newborn period, a stage II procedure at 4 to 6 months of age, and Fontan procedure at 18 to 36 months. The Norwood procedure remains one of the highest risk procedures in congenital heart surgery. A few small nonrandomized studies of a novel approach to the Norwood procedure have reported improved outcomes. This new approach uses a RV-to-PA shunt to provide pulmonary blood flow rather than the standard MBTS. This multi-center, randomized clinical trial will evaluate early and intermediate-term outcomes for patients undergoing a Norwood procedure with either the RV-to-PA shunt or the MBTS.
This study has been approved by the Institutional Review/Research Ethics Boards of all participating clinical centers:
Hospital for Sick Children, Toronto, Canada
Children's Hospital Boston, Boston, MA
Columbia College of Physicians and Surgeons, New York, NY
Children's Hospital of Philadelphia, Philadelphia, PA
Duke University Medical Center, Durham, NC
Brody School of Medicine at East Carolina University, Greenville, NC
Wake Forest Baptist Medical Center, Winston Salem, NC
Medical University of South Carolina, Charleston, SC
Children's Hospital of Wisconsin, Milwaukee, WI
University of Michigan, Ann Arbor, MI
Cincinnati Children's Hospital Medical Center, Cincinnati, OH
Children's Hospital of Los Angeles, Los Angeles, CA
Egleston Children's Hospital, Emory University, Atlanta, GA
Congenital Heart Institute of Florida, University of South Florida, St. Petersburg, FL
Alfred I. duPont Hospital for Children, Wilmington, DE
DESIGN NARRATIVE:
This is a prospective, randomized clinical trial of the RV-to-PA shunt versus MBTS in patients undergoing a Norwood procedure.
Study design
- Primary purpose
- Treatment
- Allocation
- Randomised
- Intervention model
- Parallel groups
- Masking
- None (open label)
- Number of arms
- 2
| Arm | Type | Receives |
|---|---|---|
| MBTS | Active comparator | Procedure: Blalock-Taussig pulmonary artery shuntBlalock-Taussig pulmonary artery shunt |
| RVPAS | Active comparator | Procedure: Right ventricular to pulmonary artery shuntRight ventricular to pulmonary artery shunt |
Who may qualify
- Sex
- All
- Healthy volunteers
- Not accepted
- Age groups
- Child, Adult, Older adult
Key inclusion criteria (3 listed)
- Diagnosis of hypoplastic left heart syndrome or related single, morphologic right ventricle anomaly
- Planned Norwood procedure
- Informed consent of parent(s) or legal guardian
Key exclusion criteria (3 listed)
- Single, morphologic left ventricle anomaly
- Preoperative identification of anatomy rendering either an MBTS or an RV-to-PA shunt technically impossible
- Any major congenital abnormality (i.e., congenital diaphragmatic hernia, tracheoesophageal fistula) or acquired extra-cardiac disorder (e.g., meconium aspiration with need for high frequency ventilation, persistent renal failure requiring dialysis) that, in the opinion of the investigator, could independently affect the likelihood of the subject meeting the primary endpoint
Eligibility is decided by the study team after screening; this overview does not establish that a patient qualifies. Full inclusion and exclusion criteria.
Interventions
| Intervention | Type | Arms |
|---|---|---|
| Blalock-Taussig pulmonary artery shuntAlso: MBTS procedurePerformed at stage I palliative surgery for babies born with HLHS | Procedure or surgery | MBTS |
| Right ventricular to pulmonary artery shuntAlso: RV to PA or Sano procedurePerformed at stage I palliative surgery for babies born with HLHS | Procedure or surgery | RVPAS |
Primary outcome
Proportion of Patients Who Died or Received a Heart Transplant
Time frame: Measured at 12 months
The primary outcome was the proportion of patients who died or had cardiac transplantation 12 months after randomization.
16 secondary outcomes
Proportion of Deaths or Heart Transplants Over Time From Randomization to the End of the Trial
Time frame: From Randomization to the End of the Trial, an average of 32 months
Echocardiographic Measures of Heart Size and Function: Right Ventricle (RV) End-diastolic Volume Indexed to Body Surface Area (BSA)
Time frame: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV End-diastolic Volume Indexed to BSA
Time frame: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV End-diastolic Volume Indexed to BSA
Time frame: Measured at 14 months of age
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Time frame: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Time frame: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV End-systolic Volume Indexed to BSA
Time frame: Measured at 14 months of age
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Time frame: Measured post-Norwood, an average of 17 days post-Norwood
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Time frame: Measured pre-stage II surgery, an average of 15 days pre-stage II surgery
Echocardiographic Measures of Heart Size and Function: RV Ejection Fraction
Time frame: Measured at 14 months of age
Angiographic Findings: Left Pulmonary Artery Size
Time frame: Measured pre-stage II surgery, on average 26 days prior to stage II palliation
Angiographic Findings: Right Pulmonary Artery Size
Time frame: Measured pre-stage II surgery, on average 26 days prior to stage II palliation
Unintended Cardiovascular Interventional Procedures
Time frame: From Randomization to 12 months
Complications: Total Number Experienced During Norwood Hospitalization
Time frame: Norwood Hospitalization, an average of 36 days
Complications: Total Number Experienced From Norwood Discharge to Stage II Discharge
Time frame: From Norwood Discharge to Stage II discharge, an average of 4.2 months
Complications: Total Number Experienced From Stage II Discharge to 14 Months of Age
Time frame: From Stage II Discharge to 14 Months of Age, an average of 8.9 months
Results and safety
Loading the posted results from ClinicalTrials.gov…
Research links
- Official record on ClinicalTrials.govLast updated by the sponsor 11 Mar 2025.
- Posted resultsParticipant flow, baseline, all outcome measures and adverse events.
- Background: PubMed 18954638Ohye RG, Gaynor JW, Ghanayem NS, Goldberg CS, Laussen PC, Frommelt PC, Newburger JW, Pearson GD, Tabbutt S, Wernovsky G, Wruck LM, Atz AM, Colan SD, Jaggers J, McCrindle BW, Prakash A, Puchalski MD, Sleeper LA, Stylianou MP, Mahony L; Pediatric Heart Network Investigators. Design and rationale of a randomized trial comparing the Blalock-Taussig and right ventricle-pulmonary artery shunts in the Norwood procedure. J Thorac Cardiovasc Surg. 2008 Oct;136(4):968-75. doi: 10.1016/j.jtcvs.2008.01.013. Epub 2008 May 19.
- Results publication: PubMed 21331516Johnson JN, Ansong AK, Li JS, Xu M, Gorentz J, Hehir DA, del Castillo SL, Lai WW, Uzark K, Pasquali SK. Celiac artery flow pattern in infants with single right ventricle following the Norwood procedure with a modified Blalock-Taussig or right ventricle to pulmonary artery shunt. Pediatr Cardiol. 2011 Apr;32(4):479-86. doi: 10.1007/s00246-011-9906-y. Epub 2011 Feb 18.
- Results publication: PubMed 21397260Virzi L, Pemberton V, Ohye RG, Tabbutt S, Lu M, Atz TC, Barnard T, Dunbar-Masterson C, Ghanayem NS, Jacobs JP, Lambert LM, Lewis A, Pike N, Pizarro C, Radojewski E, Teitel D, Xu M, Pearson GD. Reporting adverse events in a surgical trial for complex congenital heart disease: the Pediatric Heart Network experience. J Thorac Cardiovasc Surg. 2011 Sep;142(3):531-7. doi: 10.1016/j.jtcvs.2010.11.052. Epub 2011 Mar 12.
- Results publication: PubMed 20561642Atz AM, Travison TG, Williams IA, Pearson GD, Laussen PC, Mahle WT, Cook AL, Kirsh JA, Sklansky M, Khaikin S, Goldberg C, Frommelt M, Krawczeski C, Puchalski MD, Jacobs JP, Baffa JM, Rychik J, Ohye RG; Pediatric Heart Network Investigators. Prenatal diagnosis and risk factors for preoperative death in neonates with single right ventricle and systemic outflow obstruction: screening data from the Pediatric Heart Network Single Ventricle Reconstruction Trial( *). J Thorac Cardiovasc Surg. 2010 Dec;140(6):1245-50. doi: 10.1016/j.jtcvs.2010.05.022. Epub 2010 Jun 18.
- Results publication: PubMed 20505177Ohye RG, Sleeper LA, Mahony L, Newburger JW, Pearson GD, Lu M, Goldberg CS, Tabbutt S, Frommelt PC, Ghanayem NS, Laussen PC, Rhodes JF, Lewis AB, Mital S, Ravishankar C, Williams IA, Dunbar-Masterson C, Atz AM, Colan S, Minich LL, Pizarro C, Kanter KR, Jaggers J, Jacobs JP, Krawczeski CD, Pike N, McCrindle BW, Virzi L, Gaynor JW; Pediatric Heart Network Investigators. Comparison of shunt types in the Norwood procedure for single-ventricle lesions. N Engl J Med. 2010 May 27;362(21):1980-92. doi: 10.1056/NEJMoa0912461.
- Results publication: PubMed 17308942Ohye RG, Devaney EJ, Hirsch JC, Bove EL. The modified Blalock-Taussig shunt versus the right ventricle-to-pulmonary artery conduit for the Norwood procedure. Pediatr Cardiol. 2007 Mar-Apr;28(2):122-5. doi: 10.1007/s00246-006-1449-2. Epub 2007 Feb 16.
- Derived from this study: PubMed 41811273Hill KD, Kang L, Wang Q, Newburger JW, Gaynor JW, Burns KM, Williams R, Trachtenberg F, McCrindle BW, Graham EM, Pizarro C, Ashfaq A, Souza A, Kuo JA, Ilardi D, Schumacher KR, Hong H, Goldberg CS; Pediatric Heart Network Investigators. Single-Ventricle Disease: Long-Term Outcomes and Global Morbidity in the Single Ventricle Reconstruction Trial. J Am Coll Cardiol. 2026 Jun 9;87(22):3114-3133. doi: 10.1016/j.jacc.2026.01.049. Epub 2026 Mar 11.
- Derived from this study: PubMed 41706109Cnota JF, Chowdhury SM, Floh A, Gongwer R, Goot BH, Jacobs JP, Jolley MA, Kirmani S, LaPar DJ, Levine JC, Lewis AB, Pignatelli RH, Pizarro C, Slesnick TC, Thorsson T, Trachtenberg F, Truong DT, Newburger JW, Frommelt PC; Pediatric Heart Network Investigators. Tricuspid Regurgitation and Impact of Surgical Valve Intervention in the Single Ventricle Reconstruction Trial. Pediatr Cardiol. 2026 Feb 18. doi: 10.1007/s00246-025-04122-x. Online ahead of print.
- Derived from this study: PubMed 37866470Mahle WT, Keesari R, Trachtenberg F, Newburger JW, Lim H, Edelson J, Jeewa A, Lal A, Kindel SJ, Burns KM, Lang S, Bainton J, Carboni M, Villa CR, Richmond M, Henderson H, Menteer J, Pizarro C, Goldberg CS. School age and adolescent heart failure following the Norwood procedure. J Heart Lung Transplant. 2024 Mar;43(3):453-460. doi: 10.1016/j.healun.2023.10.012. Epub 2023 Oct 20.
- Derived from this study: PubMed 36073629Dolgner SJ, Tjoeng YL, Chan T. Analysis of the Single Ventricle Reconstruction Trial Using Restricted Mean Survival Time and Shunt Type Received. J Am Heart Assoc. 2022 Sep 20;11(18):e025978. doi: 10.1161/JAHA.122.025978. Epub 2022 Sep 8. No abstract available.
- Derived from this study: PubMed 30979811Miller TA, Ghanayem NS, Newburger JW, McCrindle BW, Hu C, DeWitt AG, Cnota JF, Tractenberg FL, Pemberton VL, Wolf MJ, Votava-Smith JK, Fifer CG, Lambert LM, Shah A, Graham EM, Pizarro C, Jacobs JP, Miller SG, Minich LL; Pediatric Heart Network Investigators. Gestational Age, Birth Weight, and Outcomes Six Years After the Norwood Procedure. Pediatrics. 2019 May;143(5):e20182577. doi: 10.1542/peds.2018-2577. Epub 2019 Apr 12.
- Derived from this study: PubMed 30755054Frommelt PC, Hu C, Trachtenberg F, Baffa JM, Boruta RJ, Chowdhury S, Cnota JF, Dragulescu A, Levine JC, Lu J, Mercer-Rosa L, Miller TA, Shah A, Slesnick TC, Stapleton G, Stelter J, Wong P, Newburger JW. Impact of Initial Shunt Type on Echocardiographic Indices in Children After Single Right Ventricle Palliations. Circ Cardiovasc Imaging. 2019 Feb;12(2):e007865. doi: 10.1161/CIRCIMAGING.118.007865.
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Referral and contact
AzTrials does not enrol participants or take referrals. Contact the study team or a site listed below; they decide who can take part. This study is not recruiting at the moment.
Julie E Miller, MPH principal investigator
New England Research Institutes, Watertown, MA
13 sites in 2 countries: see every site and its status.
Questions about this trial
What is this clinical trial studying?
A study testing Blalock-Taussig pulmonary artery shunt and Right ventricular to pulmonary artery shunt in people with Heart Defects, Congenital, run by Carelon Research at 13 sites in 2 countries.
The full registered description is in the About this study section and the official record.
Who may be eligible to take part?
The sponsor lists 3 inclusion and 3 exclusion criteria. Eligibility is decided by the study team after screening, so read the full criteria and contact a listed site.
Is this clinical trial currently recruiting?
The record says: finished, as of the sponsor's last update on 11 Mar 2025. Status can change between updates, so confirm with the study contact before making plans.
Where is the study taking place?
The record lists 13 sites in United States, Canada. Whether a site is taking part right now should be confirmed with that site. See every site.
What are the possible benefits and risks?
They depend on the study and the treatment, and no study can promise a benefit. The study team explains the known risks during informed consent, before anyone joins; the record itself does not list them.
Are results available for this study?
Yes. Results are posted in the registry (first posted 27 Jun 2011). A summary is in the For doctors view, and the full results are on ClinicalTrials.gov.
How can a doctor refer a patient or contact the research team?
The record lists no contact. The official record names the sponsor, who can be asked directly. AzTrials does not enrol participants or take referrals.
What does the primary outcome measure?
Proportion of Patients Who Died or Received a Heart Transplant (time frame: Measured at 12 months). It is what the study was designed to measure, not a finding.
Where can I read the original study information?
On the ClinicalTrials.gov record for NCT00115934, which also lists 38 linked publications.
Does a listing mean the treatment is approved or proven to work?
No. A listing means the study is registered. It does not show that the treatment is safe, works, or is approved by a regulator.
How often is this information updated?
AzTrials copies changed records from ClinicalTrials.gov every night and reloads the whole registry every week. The sponsor last updated this record on 11 Mar 2025.